Anestesia venosa total em paciente portador de Osteogênesis imperfecta. Relato de caso

Abstract

BACKGROUND AND OBJECTIVES:OsteogenesisImperfecta is an uncommon genetic connective tissue diseasewith prevalence of 1/10000, primarily involving endochondralossification, resulting in brittle bones, multiple fractures andskeletal deformities. This article aimed at reporting a case ofOsteogenesis Imperfecta patient submitted to total intravenousanesthesia for fractured femur surgical repair.CASE REPORT:Male patient, 15 years old, 41 kg, 140 cm, withhistory of Osteogenesis Imperfecta and cardiopathy, scheduledfor fractured femur surgical repair. In the operating room patientwas monitored with ECG, HR, NIBP and SpO2and was submit-ted to total intravenous anesthesia with propofol, alfentanil andcisatracurium. Monitoring of PETCO2and esophageal tempera-ture was introduced after TI. There have been no complicationsboth in the intraoperative periodand in the post-anesthetic careunit. Patient was discharged 5 days later.CONCLUSIONS:This report has shown satisfactory intra andpostoperative evolution of Osteogenesis Imperfecta patientsubmitted to total intravenous general anesthesia. Diseasecomplexity has shown the need for anesthesiologist’s adequateevaluation and monitoring.